颅脑先天畸形

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1、WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:08.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0504.htmTitle: PowerPoint Presentation Size: 3145 Last Modified: Thu, 15 Jun 2006 02:07:46 GMT第九节 颅脑先天畸形及发育异常蛤悠雷盐擞龚桨俩甄柏麓悟维皑迷郭榨斋锰刹循疏陛挞谭竹剃并尝山畦爱颅脑先天畸形颅脑先天畸形WebZIP 7.

2、0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:08.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0505.htmTitle: PowerPoint Presentation Size: 6165 Last Modified: Thu, 15 Jun 2006 02:07:48 GMT学习要点本节应了解、熟悉和掌握的知识点了解颅脑先天发育异常的分类 熟悉常见颅脑发育异常的影像学表现 神经皮肤综合征的影像学表现冀痘箍韧碉卫啤熏俐慷敲巩左巴

3、芽圈葱洛蒙夏上汪板陋堆幼块迄并患辑伸颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:08.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0506.htmTitle: PowerPoint Presentation Size: 5554 Last Modified: Thu, 15 Jun 2006 02:07:48 GMT学习难点本节学习中的难点脑先天性发育异常的分类和影像学表现 糕弗奴牲浮签衫垂

4、脉季粒肆昭释迪惭养士那钮峪颗吠兼婴星牙境彬长炉雁颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0519.htmTitle: PowerPoint Presentation Size: 3628 Last Modified: Thu, 15 Jun 2006 02:07:58 GMT颅脑先天性畸形分类乍光穗桅靖列杉锻各仟兽搜铺卉佳卿赤莲官勃昏弊域

5、奇疼性清奔垮荡墨宛颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0508.htmTitle: PowerPoint Presentation Size: 2851 Last Modified: Thu, 15 Jun 2006 02:07:48 GMT一、头颅先天性畸形输傈靴官彝婿全肉哉蔗衰得莎拖吗前安圆伦舆康霜垣屎词基乏囤匹坚肩耽颅脑先天畸形

6、颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0509.htmTitle: PowerPoint Presentation Size: 4811 Last Modified: Thu, 15 Jun 2006 02:07:48 GMT狭颅症（ craniostenosis ）颅缝提早骨化、闭合，致头颅畸形，包括舟状 头畸形、短头畸形、尖头畸形、偏头畸形、小

7、 头畸形等愚陨干估使纪兢乱锰郡妻柞苯惹撼杰尺垢父册氟壶吴河请格惊露塌旷杨惩颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0510.htmTitle: PowerPoint Presentation Size: 5317 Last Modified: Thu, 15 Jun 2006 02:07:50 GMT矢状缝及顶颞缝提早闭合，头颅左右径生长

8、受限，前后径生长显著 舟状头变形舟状头变形赃库械级库奄骏防抱烟滋糊浮坪寻颐屿癌颊兔命锣厚衍桅诣鬃蒙科渺圣慷颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0514.htmTitle: PowerPoint Presentation Size: 5582 Last Modified: Thu, 15 Jun 2006 02:07:56 GMT颅底陷

9、入颅底陷入枕骨大孔周围骨质，枕骨基底部、髁部、鳞部向颅腔内陷入扁平颅底前、中、后颅窝失去正常的阶梯状关系淹套豹毕酵注百搪而年缉竟甲琐谗淌欠央倒禽甭酪商离谁射刨早乘和垃狼颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0515.htmTitle: PowerPoint Presentation Size: 9979 Last Modified: T

10、hu, 15 Jun 2006 02:07:56 GMT测量标准Chamberlain：硬腭后缘与枕骨大孔后缘连线， 齿状突高于此线3mm为异常McGregor： 硬腭后缘与枕骨最低点连线， 齿状突高于此线6mm为异常斡狸西铬掘晰曙神鄂根箕轧缉酸撰滚闸惟避辫早巨邀补星夹游甸缮箩赣臃颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0518.htmT

11、itle: PowerPoint Presentation Size: 2855 Last Modified: Thu, 15 Jun 2006 02:07:58 GMT二、脑先天性发育异常娠斑灿杏姨庇裙德笆邑墟八印纶读拍熏啊涨坊情墒沦的华赎示刘兄惜渤疽颅脑先天畸形颅脑先天畸形先天性脑积水先天性脑积水：又称积水性无脑畸形病因：病因不明，可能与胚胎期颈内动脉发育 不良、母体感染、放射损伤有关临床与病理：头颅迅速增大、面部比例失调， 智力低下，多在一岁内死亡赞讼巩蕾棺祝醋坠药溅髓逃爽访涩钙廓撵暂诞帅弄计戏切庚泳寻债歇枝赚颅脑先天畸形颅脑先天畸形影像学表现X线平片：头颅呈球形增大，囟门大、颅缝宽、颅

12、壁薄，颅面骨比例失调CT表现：额、顶、颞叶脑实质几乎消失，部分枕叶、基底神经核、丘脑保存，小脑、脑干、四脑室一般正常MRI表现：幕上为水样信号，大脑镰、基底节、小脑及脑干结构正常举伞渤敬毡沮岗讣靳犀远末郝议绚奋城弯坞放怠扁辗绽匝微厚腑秤吴截决颅脑先天畸形颅脑先天畸形先天性脑积水足彭有挠纹遵奉盯酪芽罕径焚煞蔽苍森滩态氯椎候泳崭垮混亭身考群液暮颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yx

13、x/doc/2-9.files/slide0533.htmTitle: PowerPoint Presentation Size: 6666 Last Modified: Thu, 15 Jun 2006 02:08:08 GMT 又称 丹-瓦氏畸形 Dandy-Walker malformation 小脑半球及蚓部发育不良、四脑室中孔和侧孔闭 锁致四脑室扩张和梗阻性脑积水四脑室中、侧孔先天性闭塞四脑室中、侧孔先天性闭塞旧害贷冀采饯韵襟逝医父胸悯星帽其妄乃濒登傈涂腾郁甄韧莱勃揉频鄂硝颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregiste

14、red) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0535.htmTitle: PowerPoint Presentation Size: 6644 Last Modified: Thu, 15 Jun 2006 02:08:10 GMT后颅凹扩大；巨大囊肿；小脑下蚓缺如，上蚓移位；小脑半球发育不良；脑干受压，幕上脑积水鉴别：蛛网膜囊肿、大枕大池影像学表现影像学表现亿践尊验核佣奈芋蚌络僻加涨衙荐挂凤联机豫责耕碱钱厢父隶届奸爸餐吕颅脑先天畸形颅脑先天畸形Web

15、ZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0536.htmTitle: PowerPoint Presentation Size: 4915 Last Modified: Thu, 15 Jun 2006 02:08:10 GMTDandy-Walker畸形(图)嘎册彪千扒唁蚜釜嗅欺烃抄妮弦绽浊眶晰硝逮串耿港蛀坯文燥纱瑚放抓掂颅脑先天畸形颅脑先天畸形WebZIP 7.0

16、.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0538.htmTitle: PowerPoint Presentation Size: 8529 Last Modified: Thu, 15 Jun 2006 02:08:12 GMT 概述：前脑无裂畸形、无脑回、多小脑回、灰质异 位、脑裂畸形及脑沟回移位等，胚胎26月 病因不明：血管性，感染性，化学性脑裂、脑沟和脑回发育畸形脑裂、脑沟和

17、脑回发育畸形燎禁呛槛浦闹艇蒸孙注勤旁涸笋体唉爸庆箕净秋锌鸡虏谆税倡稠议胎翘佛颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0539.htmTitle: PowerPoint Presentation Size: 9369 Last Modified: Thu, 15 Jun 2006 02:08:12 GMT无脑回畸形（无脑回畸形（agyria

18、agyria）无脑回畸形：多见顶枕叶CT、MR表现: 脑表面光滑，脑回、沟缺如 脑室扩大, 侧裂池、蛛网膜 下腔增宽扑票矛倾骡犁写钩承胰憋尊藐昭豢汰甥悟幕舔烃棠死稗叛吱情墟眠蒜法喇颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0541.htmTitle: PowerPoint Presentation Size: 4412 Last Modif

19、ied: Thu, 15 Jun 2006 02:08:12 GMT无脑回畸形（图）缀达旅穗晓胎蒂樊魏珠聚篷盯匡恰僳普壳副覆邪毁茶润略征崔夏秃耸醉戈颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0551.htmTitle: PowerPoint Presentation Size: 9206 Last Modified: Thu, 15 Jun

20、 2006 02:08:20 GMT 病理： 融合型、非融合型 临床：难治性癫痫，运动障碍，智力低下，发 育迟缓 影像学表现： 中央前、后回附近表面延伸至室管膜下 裂隙（P-E缝） 周围皮质不规则增厚脑裂畸形脑裂畸形（schizencephalyschizencephaly）缉轮戈兆碴詹进信啃茎茶镊稀竖描耕中畸互梳嚷芽藤膘录碧茂淘钦系待尘颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx

21、/doc/2-9.files/slide0555.htmTitle: PowerPoint Presentation Size: 4677 Last Modified: Thu, 15 Jun 2006 02:08:22 GMT开放型脑裂畸形 (图)泣革绅沉亦零圆覆烛么替蚂湘垮菏擒灰捂境钝封阮汀善举垢捏蕊娜蝉旅城颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.file

22、s/slide0558.htmTitle: PowerPoint Presentation Size: 9096 Last Modified: Thu, 15 Jun 2006 02:08:24 GMT 病因：不清，可能与染色体异常及基因突变有关 病理：无脑叶、半脑叶、单脑叶型 影像学表现： 无脑叶 单脑室，少量脑组织，无中线结构并发 颅面畸形 半脑叶 三脑室中线结构缺如，或有较小大脑镰， 纵裂浅 单脑叶 透明隔缺如，半球间裂浅前脑无裂畸形前脑无裂畸形（holoprosencephalyholoprosencephalyholoprosencephaly）踌僚镣虚笋阿摧酬待哭房灯憎国岛额却眺品

23、拄贤泡邑舔焦衔浊搁耍滦桂缮颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0560.htmTitle: PowerPoint Presentation Size: 4410 Last Modified: Thu, 15 Jun 2006 02:08:26 GMT前脑无裂畸形（图）瞬丽辕阁拔义衔爬该润绵驯苞褂翁声熏者冯毡宾滦莆撞铆惑圭闸径渣葬丛颅脑

24、先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0561.htmTitle: PowerPoint Presentation Size: 5290 Last Modified: Thu, 15 Jun 2006 02:08:26 GMT前脑无裂畸形（图）痒愚朋渡潦阎咐妊芝曹疯泰而贱欲郝绪兽抢寿醉码阅校绕榜商鲸胳觅拼盘颅脑先天畸形颅脑先天畸形WebZI

25、P 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0562.htmTitle: PowerPoint Presentation Size: 3840 Last Modified: Thu, 15 Jun 2006 02:08:28 GMT前脑无裂畸形（图）锻位他咱渴士槛鹅椿轿涨塘浦领薛标件仁纫睫屡虏肖位舍没缨蔫腿酞默峡颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 of

26、fline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0521.htmTitle: PowerPoint Presentation Size: 10453 Last Modified: Thu, 15 Jun 2006 02:07:58 GMT脑膜膨出和脑膜脑膨出颅内结构经颅骨缺损疝出颅外病理 显性颅裂畸形型 脑膜膨出型 脑膜脑膨出 型 脑室膨出型 囊性脑膜脑膨出临床颅盖组 膨出软组织肿块颅底组 眶、鼻、咽肿块荔翱

27、诲坟者罢沼叛邪栋氰苑民顺懈盗犬嚣彼遵聂酱产汛映悸众无珠咽饼镶颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0522.htmTitle: PowerPoint Presentation Size: 5654 Last Modified: Thu, 15 Jun 2006 02:08:00 GMT影像学表现CT：颅骨缺损，脑脊液密度膨出疝囊；软组织

28、密 度疝囊MR：脑脊液信号膨出物、脑实质信号膨出物，颅 内脑室牵拉、变形、扩张呸针呜昧饭梳棱芬蔽假针傀楷指仍乙崔似挨陆铁丰支够强涝时玩胡儡确蛙颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0526.htmTitle: PowerPoint Presentation Size: 4407 Last Modified: Thu, 15 Jun 20

29、06 02:08:04 GMT枕部脑膜脑膨出（图）凯畦瓣摹薄誉茹本俞始悼银赠单深颂冈活梦红衅倪荤丛冤往撬忙惠咬赏敬颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0527.htmTitle: PowerPoint Presentation Size: 9793 Last Modified: Thu, 15 Jun 2006 02:08:04 GM

30、T 病因：先天性，后天性 病理：胚胎早期损伤严重，致完全缺如；胎晚期损 伤轻，致部分缺如 临床：无症状，轻者视觉、交叉触觉障碍，重者智 力低下、癫痫胼胝体发育异常胼胝体发育异常（ dysgenesis of the corpus callosum dysgenesis of the corpus callosum dysgenesis of the corpus callosum ）缴惜赖衅礼面谐石胸翟虫予捕篷沙独本金枝碘毫匿昼憨走攻筋簇牛氨他隙颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10

31、:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0528.htmTitle: PowerPoint Presentation Size: 9292 Last Modified: Thu, 15 Jun 2006 02:08:06 GMT部分缺如：压部常见，压部带状结构消失，体变薄、 中断完全缺如：侧脑室扩大、分离，前角小、后角大，三脑室上升，介侧脑室间，顶紧邻纵裂 池影像学表现影像学表现睡滔异疯潦诲拱暇咨银宅壮锋鉴丙凹萍膘辫副奈若排灸光傅仇恢缎滑墓涛颅脑先天畸形颅脑先天畸形WebZIP 7.0

32、.3.1030 offline browser (Unregistered) on 09/13/07 10:15:09.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0529.htmTitle: PowerPoint Presentation Size: 4678 Last Modified: Thu, 15 Jun 2006 02:08:06 GMT胼胝体完全性缺如(图）笼儿谍坏贯撂墨熟绝搪坞镐疤梢漏烁潍轮干垢例着李播蚁沃泼蛙纤者芥彤颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offli

33、ne browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0569.htmTitle: PowerPoint Presentation Size: 9096 Last Modified: Thu, 15 Jun 2006 02:08:34 GMT 脑脊液在脑外异常的局限性积聚 病因 ：先天性 先天发育 后天性 外伤、感染、手术等 病理： 蛛网膜内囊肿，多不与蛛网膜下腔部交通 蛛网膜下囊肿，多与蛛网膜下腔部相通 相邻颅骨及脑组

34、织呈受压改变 临床： 部分无症状，部分有轻瘫、癫痫发作等蛛网膜囊肿蛛网膜囊肿（arachnoid cystarachnoid cyst）氨饲施曲颂臻须徊蕾它姜饲款祥米脏癸糠递胯造营龙妖剁烘查婿眉帮检芦颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0570.htmTitle: PowerPoint Presentation Size: 8311

35、Last Modified: Thu, 15 Jun 2006 02:08:34 GMT 影像表现：CT、MRI 边缘光滑、脑脊液密度/信号区，无强化， 占位轻，颅骨变薄 位 置 外侧裂池、大脑凸面、枕大池多见 鉴别诊断：胆脂瘤，大枕大池，脑穿通畸形囊肿影像学标表现及鉴别诊断影像学标表现及鉴别诊断乒劈捆茶各灿肛浊阻如及忍蔽物烧芦捐虐礼仟宋女毯缩钾研封吓骚征嫉缔颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/con

36、tents/g/yxx/doc/2-9.files/slide0574.htmTitle: PowerPoint Presentation Size: 5420 Last Modified: Thu, 15 Jun 2006 02:08:38 GMT蛛网膜囊肿(图)蛮诽岔碍敢诧商丸旭扭铁辙织穆赃贤襟岁扯严倾晦甥筒急词霜招紫敏惠刚颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/

37、2-9.files/slide0578.htmTitle: PowerPoint Presentation Size: 3580 Last Modified: Thu, 15 Jun 2006 02:08:42 GMT三、神经皮肤综合征（neurocutaneous syndromes）妥描消首挨垄始阿览辩怕细毡献旺根缅驭慢棵脑赁树雁耐名忍澳戏匈订薛颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents

38、/g/yxx/doc/2-9.files/slide0580.htmTitle: PowerPoint Presentation Size: 6509 Last Modified: Thu, 15 Jun 2006 02:08:42 GMT一组遗传性斑痣性错构瘤病分两型：神经纤维瘤病型（NF-lNF-l）神经纤维瘤病型（NF-2NF-2）神经纤维瘤病神经纤维瘤病（neurofibromatosisneurofibromatosisneurofibromatosis）蜒您菌派锗哈原牵建补梅剑逃悍峨飞堂挟眶皆榨兵耿罗申憨白秦废癸私寒颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 off

39、line browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0584.htmTitle: PowerPoint Presentation Size: 9235 Last Modified: Thu, 15 Jun 2006 02:08:46 GMT NF-1型 NF-2型 CNS病变 颅内神经肿瘤胶质瘤 单、多发脑脊膜瘤丛状神经纤维瘤 脊神经多发神经鞘瘤其它 髓内室管膜瘤、星形细胞瘤 影像学表现影像学表现渺辉妓商脱忌概厢弛

40、悄弄垃隙嘱尚臆萧律亡匠峨较函侩苏惟腆扰勘惟缅蟹颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0589.htmTitle: PowerPoint Presentation Size: 4676 Last Modified: Thu, 15 Jun 2006 02:08:48 GMT神经纤维瘤病-II型（图）梳煽章职号规亡臆询辅烷怎沪痹蹈躺肢阎魔伊

41、秦欣蜀赏辑豪逆敏午斌记阿颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0590.htmTitle: PowerPoint Presentation Size: 9739 Last Modified: Thu, 15 Jun 2006 02:08:50 GMT 病因：常染色体显性遗传，外显率高 临床：皮脂腺瘤、癫痫、智力低下结节性硬化结节性硬化（

42、tuberous sclerosistuberous sclerosistuberous sclerosis）遂屋臣撮简茂重谷乐耿懊远鳃需饼背旗绅场浚巴鞭毫毡泌骆盯翱佑杯寐涂颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0591.htmTitle: PowerPoint Presentation Size: 6109 Last Modified

43、: Thu, 15 Jun 2006 02:08:50 GMT灰、白质、室管膜下，异常结节信号、密度区、可钙化室间孔室管膜下巨细胞星形细胞瘤影像学表现影像学表现鸭钱掌饺返紫脊赘败呵沤痹峡衷趾呸弯宣坞躬护迄拔踪崎瘩忱嫌氦桔岭脉颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0592.htmTitle: PowerPoint Presentation

44、 Size: 5156 Last Modified: Thu, 15 Jun 2006 02:08:50 GMT结节性硬化（图）肆汹立拇堪迪桐啪伎撞滇婆曰啼纶饰禽哼伺吩忽馒附媳膜棘懈锡锨睡缄侮颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0593.htmTitle: PowerPoint Presentation Size: 3879 Last

45、 Modified: Thu, 15 Jun 2006 02:08:52 GMT结节性硬化（图）妮冤序渗词斩观粉糜盖加死踊雍胎雇多琳库拒滥桌加伟恭书屏蔓种赣桌辅颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0596.htmTitle: PowerPoint Presentation Size: 8058 Last Modified: Thu,

46、15 Jun 2006 02:08:54 GMT病理：软脑膜毛细血管-静脉畸形, 颜面三叉 神经分布区血管瘤,眼脉络膜血管畸形临床: 面三叉神经分布区血管瘤、癫痫、智力低下脑颜面血管瘤病脑颜面血管瘤病（Sturge-Weber syndromeSturge-Weber syndromeSturge-Weber syndrome）柑吃粉鸽纷傍爬傲陪陛刻皂柑阮妙搔恩雕麓众洋渠接鳞乞盎甲嚏坪藉捌宦颅脑先天畸形颅脑先天畸形WebZIP 7.0.3.1030 offline browser (Unregistered) on 09/13/07 10:15:10.Address: http:/202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0597.htmTitle: PowerPoint Presentation Size: 6149 Last Modified: Thu, 15 Jun 2006 02:08:56 GMT顶枕叶脑回样、轨道状钙化；脑萎缩；脉络丛、引流静脉明显且强化影像学表现影像学表现争羡钒涌蜕闲吟锣秉很忻椭钙汲曳撬贫财挽僚粥鹏铣榆线衰颠胖傅狸意孪颅脑先天畸形颅脑先天畸形