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1、(-)All(PT)Dll11135(12ls)3sHD(PTR)1.00.05 (0.82-1.15) so(INR) l.O+O.lo 1. PTI II onvxKDIC2. PTHDDICfttl3. PTRINR2.02.5HD(APTT)31_43s10s1. APTTXIIXXVIIPK HMWK Fvnk ixxiAPTT2. APTTDllAll2-4g/Lo 1 2DICDllD-D-X IIID-200yg/Lc D-DD-(DVT),(PE),(DIC) AllHDD-ffilHDD-cTnT(01UD1201206.5%4%6%:6%7%:7%8%:8%9%:9%:
2、HDAllAll(GDM)(TSH)TSHT4T3R2_10mU/Lo 1 2(T3)T4)T31.72.3nmolt T4 65156nmol/Lo 1 2(ANADNADNADNARNAANADNAANAIgG,IgM. IgA,IgDIgE ANA (MMANADNAMANASLE,SLE (HHANAHANASLE,HANA (SSmSSB/LaScl-70SANASLE,(MCTD),(PSS),(SS),(PMDM)99% (86%100%)SLEANA1: 80,ANAANAANASLEDNADNA (ds-DNA)ds-DNASLESLEds-DNA(CCP)(RA),IgGC
3、CPRACCPCCP50AU/ml 4613T36.5 C,BP120/80mniHg156cm.75KG.7622OGTT+(-)on1. (POX)miHDPOX2(NAP)NAP10%40%;4080 (1) NAP(2) NAP0NAP (3) UDNAPNAPtai(4) NAP(5) NAPNAP(6) ACTHNAP3a(a-NAE)(NaF)4PAS(1) aim(2) PAS(3) PASGaucherPAS POX “-NAE +4-“NAE+NaF NaFNaFNAPPAS 520%90%,65% (1) All15%,“0HD(2) 15%(3) (HlnoUn1 HD
4、(1) (2) 30%,(3) (4) (5) 2. UDHD (1) (2) 30%,50%,Howell-Jolly(3) (4) 3(1) 80%(2) 4All(1) (2) 230%WH02000220%(3) All(4) DU AuerAllFABM0 MP0MPO (+); CD13, CD33 (+);Ml 290%; POX (+) o M230%89%;20%oM3 f!D30%oM4 30%;20%;20%o15011B80%oM6 All50%;230%217 All30%o011L1L2L35 90%10% 6(1) FAB MDSFAB (RA)(RAS)Oil(RAEB)(RAEB-T)IC1 (CMML)HD1155,1.0xl09/L55,155202030Auer520, (2) WHO RA:flllcQRCMD:HD5%) RASRCMD-RS RAEB: RAEB-1 5%-9%) ; RAEB-II 10%19%) 5q- MDS(R-N4DS) o (3) QU Un Pelger-Huet HDIID(4) 30%50%,